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Volume 5, Issue 4 (Fall 2020)                   J Obstet Gynecol Cancer Res 2020, 5(4): 172-174 | Back to browse issues page

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Sohrabi H, Yousefi-Sharmi S R, Sohrabi R. Extensive Aplasia Cutis Congenita: A Case Report. J Obstet Gynecol Cancer Res. 2020; 5 (4) :172-174
URL: http://jogcr.com/article-1-295-en.html
1- Master's Student of Midwifery Education, Department of Midwifery, School of Nursing and Midwifery, Kurdistan University of Medical Sciences, Sanandaj, Iran
2- epartment of Obstetrics and Gynecology, School of Medicine, Kurdistan University of Medical Sciences, Sanandaj, Iran , Yousefi805@yahoo.com
3- General PhD Student, Department of Medicine, School of Medicine, Kurdistan University of Medical Sciences, Sanandaj, Iran
Abstract:   (97 Views)
Aplasia cutis congenita (ACC) is a rare congenital disorder characterized by localized or widespread skin absence. The most common site is the scalp and the main cause is unknown. Here we report a case of extensive ACC with scalp involvement. A female infant with an Apgar score of 9 and weighing 3406 gr was born by cesarean section in Besat Hospital, Sanandaj, Iran. A lesion measuring 5×10 cm with highly prominent vessels was on the forehead and parietal bone without scalp, skull, or bone tissue leading to the brain tissue being covered with a thin membrane. Other clinical examinations were normal. The newborn suffered from a ruptured aneurysm and intracerebral hemorrhage and underwent pharmacologic treatment. She died after 21 days of hospitalization. In order to prevent mortality in infants with skin defects, infection control is a priority. Antibiotics could be administered in cases with extensive lesions to prevent neonatal sepsis and improve scar tissue formation. Moreover, restorative measures should be taken if necessary.
Full-Text [PDF 316 kb]   (23 Downloads)    
Systematic Review: Case Report | Subject: Obstetrics and Gynecology
Received: 2020/06/2 | Accepted: 2020/08/29 | Published: 2020/09/8

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