Write your message
Volume 5, Issue 4 (Fall 2020)                   J Obstet Gynecol Cancer Res 2020, 5(4): 172-174 | Back to browse issues page


XML Print


Download citation:
BibTeX | RIS | EndNote | Medlars | ProCite | Reference Manager | RefWorks
Send citation to:

Sohrabi H, Yousefi-Sharmi S R, Sohrabi R. Extensive Aplasia Cutis Congenita: A Case Report. J Obstet Gynecol Cancer Res. 2020; 5 (4) :172-174
URL: http://jogcr.com/article-1-295-en.html
1- Master's Student of Midwifery Education, Department of Midwifery, School of Nursing and Midwifery, Kurdistan University of Medical Sciences, Sanandaj, Iran
2- epartment of Obstetrics and Gynecology, School of Medicine, Kurdistan University of Medical Sciences, Sanandaj, Iran , Yousefi805@yahoo.com
3- General PhD Student, Department of Medicine, School of Medicine, Kurdistan University of Medical Sciences, Sanandaj, Iran
Abstract:   (97 Views)
Aplasia cutis congenita (ACC) is a rare congenital disorder characterized by localized or widespread skin absence. The most common site is the scalp and the main cause is unknown. Here we report a case of extensive ACC with scalp involvement. A female infant with an Apgar score of 9 and weighing 3406 gr was born by cesarean section in Besat Hospital, Sanandaj, Iran. A lesion measuring 5×10 cm with highly prominent vessels was on the forehead and parietal bone without scalp, skull, or bone tissue leading to the brain tissue being covered with a thin membrane. Other clinical examinations were normal. The newborn suffered from a ruptured aneurysm and intracerebral hemorrhage and underwent pharmacologic treatment. She died after 21 days of hospitalization. In order to prevent mortality in infants with skin defects, infection control is a priority. Antibiotics could be administered in cases with extensive lesions to prevent neonatal sepsis and improve scar tissue formation. Moreover, restorative measures should be taken if necessary.
Full-Text [PDF 316 kb]   (23 Downloads)    
Systematic Review: Case Report | Subject: Obstetrics and Gynecology
Received: 2020/06/2 | Accepted: 2020/08/29 | Published: 2020/09/8

References
1. Shrager S, Voin V, Iwanaga J, Tubbs RS, Johnston. Extreame aplasia cutis congenita involving the skull. Child Nerv Syst. 2017;33(8):1395-1398. [DOI:10.1007/s00381-017-3426-x] [PMID]
2. Chessa MA, Filippi F, Patrizi A, Vollonol l, Sechi A, D'Ercole MD, Leuzzi M. Aplasia Cutis: Clinical, dermoscopic findings and management in 45 children. JEADV. 2020;1-9. [DOI:10.1111/jdv.16542]
3. Yong JY, Yang WG. Large scalp and skull defect in aplasia cutis congenita. Br J Plast Surg. 2000;619-622. [DOI:10.1054/bjps.2000.3413] [PMID]
4. Gassenmaier M, Bosmuller H, Metzler G. Aplasia cutis congenita of the scalp: Histopathologic features and clinicopathologic correlation in a case series. J Cutan Pathol. 2019;47:439-445. [DOI:10.1111/cup.13644] [PMID]
5. Alshehri W, Alfadil S, Alothri A, Abdulaziz O, Wani SH, Rabah S. Aplasia cutis congenita of the scalp with a familial pattern. 2016;1-4. [DOI:10.1155/2016/4264721] [PMID] [PMCID]
6. Magliah T, Alghamdi F. Aplasia cutis congenita: A case report. KARGER.2018;10:182-186. [DOI:10.1159/000490786] [PMID] [PMCID]
7. Winston KR, Ketch LL. Aplasia cutis congenita of the scalp, composite type: The criticality and inseparability of neurosurgical and plastic surgical management.KARGER. 2016;51:111-120. [DOI:10.1159/000442989] [PMID]
8. Bharti G, Groves L, Dovid LR, Sanger C, Argenta LC. Aplasia cutis congenita: Clinical management of a rare congenital anomaly. The Journal of Craniofacial Surgery.2011;22:159-165. [DOI:10.1097/SCS.0b013e3181f73937] [PMID]
9. Evers MJ, Steijlen PM, Hamel BJ. Aplasia cutis congenita and associated disorders. Clin Genet. 1995;47:295-301. [DOI:10.1111/j.1399-0004.1995.tb03968.x] [PMID]
10. Mesrati H, Amouri M, Chaaben H, Masmoudi A, Boudaya S, Turki H. Aplasia cutis congenita: Report of 22 cases. Int J Dermatol. 2015;54:1370-1375. [DOI:10.1111/ijd.12707] [PMID]
11. Lonie S, Hons M, Med Sci B, Phua Y, Plastics F, Burge J, et al. Technique for management of aplasia cutis congenital of the scalp with a skin allograft.2016;27:1049-1050. [DOI:10.1097/SCS.0000000000002610] [PMID]
12. Zhou J, Zheng L, Tao W. Systematic aplasia cutis congenita: A case report and review of the literature. Pathol Res Pract.2010;206:504-507. [DOI:10.1016/j.prp.2009.12.011] [PMID]
13. Mohades GH, Ameli H. Aplasia cutis congenital. Stud Med Sci. 2008;19(1):72-76.
14. Alexondros B, Dimitrios G, Elias A, Evangelis D, Andreas M, Sotirios P, et al. Aplasia cutis congenita: Two case reports and discussion of the literature. Surgical Neurology International.2017;8(1):273-278. [DOI:10.4103/sni.sni_188_17] [PMID] [PMCID]
15. Mandy Sdierz IA, Giuffre M, DE Vecchio A, Antona V, Corsello G, Piro E. Recognizable neonatal clinical features of aplasia cutis congenita. Italian Journal of Pediatrics.2020;46(25):2-6. [DOI:10.1186/s13052-020-0789-5] [PMID] [PMCID]

Add your comments about this article : Your username or Email:
CAPTCHA

Send email to the article author


© 2021 All Rights Reserved | Journal of Obstetrics, Gynecology and Cancer Research (JOGCR)

Designed & Developed by : Yektaweb | Piblisher: Farname Inc.