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Volume 3, Issue 3 (Summer 2018)                   J Obstet Gynecol Cancer Res 2018, 3(3): 129-131 | Back to browse issues page

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Hasanzadeh M, Rezaee E. Presentation of Dysgerminoma and Gonadoblastoma in a Patient with Swyer Syndrome. J Obstet Gynecol Cancer Res. 2018; 3 (3) :129-131
URL: http://jogcr.com/article-1-212-en.html
1- Obstetrics & Gynecology Department, Medicine Faculty, Mashhad University of Medical Sciences, Mashhad, Iran , -hasanzademofradm@mums.ac.ir
2- Obstetrics & Gynecology Department, Medicine Faculty, Mashhad University of Medical Sciences, Mashhad, Iran
Abstract:   (1579 Views)
Introduction: Swyer syndrome is determined by primary amenorrhea, normal external genitalia, and the presence of a vagina, uterus, and 46XY karyotype. The aim of this case report was to introduce a patient with Swyer syndrome referred with pain and an abdominal mass.
Patient Information: This case study was done in Gynecology Clinic of Ghaem Hospital in Mashhad, Iran, in 2015. A single 18-year-old woman came to the clinic with complaints of primary amenorrhea, pain, and abdominal mass underwent laparotomy. Based on her histopathology report which indicated a left ovary dysgerminoma and a right ovary gonadoblastoma, a bilateral salpingo-oophorectomy, followed by chemotherapy, was conducted. The patient was under Bleomycin, Etoposide and Platinum (BEP) chemotherapy and has been living without evidence of recurrence.
Conclusion: A genetic disorder in patients younger than 20 years with an ovarian mass and diagnosis of dysgerminoma should be rejected.
Full-Text [PDF 386 kb]   (586 Downloads)    
Systematic Review: Case Report | Subject: Obstetrics and Gynecology
Received: 2018/01/24 | Accepted: 2018/03/27 | Published: 2018/09/22

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